RHEUMATOLOGICAL SYNDROMES IN CONGENITAL UNDIFFERENTIATED CONNECTIVE TISSUE DYSPLASIA

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Issue: 
10
Year: 
2017

Professor G. Bagirova, MD; E. Sagitova, Candidate of Medical Sciences; V. Gryaznov, Candidate of Medical Sciences Orenburg State Medical University

The paper gives a clinical case of congenital pathology in a 52-year-old patient; a concurrence of undifferentiated connective tissue dysplasia, muscular dystrophy, cardiomyopathy with arrhythmias, and articular syndrome. It traces the evolution of clinical manifestations ranging from childhood to the sixth decade of life.
Keywords: 
rheumatology
limb-girdle muscular dystrophy
connective tissue dysplasia
cardiomyopathy
complex heart rhythm disorders
articular syndrome

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