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LEFT VENTRICULAR NONCOMPACTION: CLINICAL MANIFESTATIONS OF THE SYNDROME

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Issue: 
3
Year: 
2015

S. Komissarova, Candidate of Medical Sciences; T. Sevruk; I. Ustinova; E. Kovsh, Candidate of Medical Sciences Republican Research and Practical Center “Cardiology”, Minsk

Left ventricular noncompaction (LVNC) is rare form of genetically heterogeneous primary cardiomyopathy. The diagnosis, clinical manifestations, and treatment of LVNC are discussed.

Keywords: 
left ventricular noncompaction
cardiomyopathy
life-threatening arrhythmias
heart failure



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References: 
  1. Stollberg C., Finsterer J. Left ventricular hypertrabeculation noncompaction // J. Am. Soc. Echcardiogr. – 2004; 17 (1): 91–100.
  2. Oechslin E., Attenhofer-Jost C., Rojas J. Long-term follow-up of adults with isolated left ventricular noncompaction: a distinct cardiomyopathy with poor prognosis // J. Am. Coll. Cardiol. – 2000; 36: 493–500
  3. Nugent A., Daubeney P., Chondros P. et al. The epidemiology of childhood cardiomyopathy in Australia // N. Engl. J. Med. – 2003; 348: 1639–46.
  4. Nihei K., Shinomiya N., Kabayama H. et al. Wolff–Parkinson–White (WPW) syndrome in isolated noncompaction of the ventricular myocardium // Circ. J. – 2004; 68: 82–4.
  5. McKenna W., Richardson P., Bristow M. Report of the 1995 WHO/ISFC task force on the definition and classification of cardiomyopathies // Circulation. – 1996; 93: 841–2.
  6. Maron B., Towbin J., Thiene G. et al. Contemporary definitions of the cardiomyopathies // Circulation. – 2006; 113: 1807–16.
  7. Elliott P., Andersson B., Arbustini E. et al. Classification of the cardiomyopathies: from the European Society of Cardiology working group on myocardial and pericardial diseases // Eur. Heart J. – 2008; 29: 270–6
  8. Chin T., Perloff J., Williams R. et al. Isolated noncompraction of left ventricular myocardium: a study of eight cases // Circulation. – 1990; 82: 507–13.
  9. Ritter M., Oechslin E., Sutsch G. et al. Isolation noncompraction of the myocardium in adults // Mayo Clin. Proc. – 1997: 72: 26–31.
  10. Sen-Chowdnry S., McKenna W. Left ventricular noncompraction and cardiomyopathy: cause, contributor, or epiphenomenon? // Curr. Opin. Cardiol. – 2008; 23: 171–5.
  11. Sedmera D., McQuinn T. Embryogenesis of the heart muscle // Heart Fail Clin. – 2008; 4: 235–5.
  12. Ichida F., Tsubata S., Bowles K. et al. Novel gene mutations in patients with left ventricular noncompaction or Barth syndrome // Circulation. – 2001; 103: 1256–64.
  13. Hoedemaekers Y., Caliskan K., Majoor-Krakauer D. et al. Cardiac beta . myosin heavy chain defects in two families with non-compaction cardiomyopathy: linking non-compaction to hypertrophic, restrictive, and dilated cardiomyopathies // Eur. Heart J. – 2007; 28 (22): 2732–7.
  14. Stollberger C., Finsterer J. Left ventricular hypertrabeculation noncompaction // J. Am. Soc. Echocardiogr. – 2004; 17 (1): 91–100.
  15. Jenni R., Oechslin E., Van der Loo B. Isolated ventricular noncompaction of 15. the myocardium in adults // Heart. – 2007; 93: 11–5.