A CASE OF FULMINANT ANCA-NEGATIVE WEGENER’S GRANULOMATOSIS WITH PRIMARY ENT INVOLVEMENT

DOI: https://doi.org/10.29296/25877305-2018-01-25
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1
Year: 
2018

D. Fernando (1–3), Candidate of Medical Sciences; V. Shpotin (1–3), MD; A. Gostyunin(1); S. Kudaev (4) 1-Aleksandro-Mariinsk Regional Clinical Hospital, Astrakhan 2-Astrakhan State Medical University 3-Astrakhan Branch, Otorhinolaryngology Research and Clinical Center, Federal Biomedical Agency of Russia 4-Postmortem Examination Bureau, Astrakhan

The paper describes a rare case of ANCA-negative Wegener's granulomatosis with a severe, fulminant course, which is manifested by primary ENT involvement.
Keywords: 
rheumatology
Wegener’s granulomatosis
granulomatosis with polyangiitis
antineutrophil cytoplasmic antibodies (ANCA)

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